Funny dubbing survival and trend Celine Dion (NOW Gal Hilleli)
The singer Celine Dion announced today (Thursday) that she had to cancel her international concert tour, which was supposed to come to Israel as well, all because she contracted a rare syndrome called the Stiff Man Syndrome.
So what is the rare syndrome and what are the treatments offered today to treat it?
Stiff person syndrome, or Mursha-Waltman syndrome (named after the doctors who discovered it in 1956), is a rare disorder characterized by stiffening of the body's muscles and muscle spasms, resulting in severe impairment of the mobility of those who suffer from it.
In severe cases, the disease can prevent movement and walking completely, and cause convulsions, convulsions and increased sensitivity to light and sound.
The rare syndrome occurs in one in a million people, mostly middle-aged women.
The syndrome is divided into three types: paraneoplastic type (when it is a patient with a malignant disease in which the syndrome develops secondary to the disease), idiopathic type (when the cause is unknown) and autoimmune type.
When it comes to an autoimmune disease, i.e. a situation where the body's immune system attacks the body itself, the rigid person syndrome may appear in combination with other autoimmune diseases such as thyroid diseases, vitiligo and especially with type 1 diabetes.
A complex and rare disease.
Celine Dion (photo: splash)
The severity and progression of the disease can vary from one person to another.
Symptoms usually develop over a period of months and may remain stable for many years or slowly worsen.
In some people, the symptoms can be stabilized with medication.
How are you treated?
People with SPS respond to high doses of several anticonvulsants.
A recent study funded by the International Society of Neurological Diseases and Stroke (NINDS) demonstrated the effectiveness of intravenous immunoglobulin (IVIg) therapy in reducing stiffness and sensitivity to noise, touch and stress in people with this syndrome.
Treatment with IVIg, anti-anxiety medications, muscle relaxants, anticonvulsants, and pain relievers will improve the symptoms of SPS, but will not cure the disorder.
Most people with SPS have frequent falls and because they lack normal protective reflexes, injuries can be severe.
With appropriate treatment, symptoms are usually well controlled.
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