A 14-year-old boy who was studying at Hong Chi Pine Ridge School in Tai Po and was suffering from chronic childhood sclerosis was fed milk and water at school on Thursday (24th). He was found fainted more than an hour later and sent to the hospital for confirmation die.
Pediatrician Wu Yongqiang explained that this disease is a rare genetic disease with a very low incidence rate, and it is difficult to have one case in 2 million people.
Affected by X-chromosomal genetic factors, the patient's brain cannot secrete lipid-like proteins that protect the brain's nerve lines, resulting in developmental delay, limb weakness, and epileptic convulsions. There is currently no targeted treatment plan.
The boy was sent to Tai Po Nethersole Hospital for emergency treatment.
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It is understood that the boy has suffered from chronic childhood sclerosis since birth.
At about 11 a.m. on the day of the incident, the boy was fed milk and water. There was no abnormality at the time, and then he watched TV in the room.
More than an hour later, the boy was found pale and unconscious on the wheelchair by the teaching staff. They immediately notified the staff to call the police for help, and the nurse gave first aid.
The boy was sent to Alice Ho Miu Ling Nethersole Hospital, where he was certified dead at 1:48 pm.
Patients are mainly male and belong to a type of dementia
Pediatrician Wu Yongqiang said that chronic childhood cerebral sclerosis is a rare disease, and it is difficult to have one patient per 1 million to 2 million people.
The cause is mainly affected by X-chromosomal genetic factors, and the main patients are male.
He then explained that 2 to 3 years after the baby is born is the most important stage for the development of brain nerves.
In this type of patients, because they cannot secrete lipoid proteins that protect the nerve lines of the brain, it is difficult for the brain to "lay the wires", so they cannot transmit information to the limbs, which is a type of dementia.
Wu Yongqiang also pointed out that most of the patients' onset time is from birth to 3 years old, and the most common symptom is developmental delay. Generally, babies will respond to external stimuli and know how to look at people after two months of birth.
After 4 months of birth, they can turn around, raise their heads, and crawl.
And half a year after birth, he was able to babble.
Patients generally do not keep up with the developmental process, so it can be diagnosed in infancy.
The average patient’s life expectancy is no more than 10 years old. There is currently no targeted treatment, and the patient’s brain will only continue to deteriorate, such as difficulty in swallowing, breathing, limb weakness, and epileptic convulsions.
Once the patient's airway is blocked by food and vomit, it is fatal.
A 14-year-old student from Hong Chi Pine Ridge School collapsed and died after being sent to hospital.
(Hong Chi Association website)
14-year-old boy suspected of fainting while watching TV in school, sent to hospital and later confirmed dead
